The article deals with VACTERL association, particularly non randomly associated birth defects, typically defined by the presence of at least three of the following congenital malformations: vertebral anomalies, anal atresia, cardiac malformations, tracheo-esophageal fistula, renal anomalies, and limb abnormalities. Museum collection of the Department of Pathological Anatomy of Kharkiv National Medical University, which devoted to prenatal and perinatal pathology, has numerous museum exhibits representing this pathology. The specimens help to discuss pathological anatomy of each of these defects.

KeyWords:  fetus, VACTERL, congenital defect.

Курчанова Ю.В., Івантеєва Ю.І., Гаргін В.В.


Статья посвящена синдрому VACTERL - закономерно объединенным врожденным патологиям развития. Для постановки синдрома необходимо присутствие не менее трех из следующих дефектов: аномалии позвоночника, анальная атрезия, пороки сердца, трахеопищеводный свищ, почечные аномалии и аномалии конечностей. Музейная коллекция кафедры патологической анатомии ХНМУ, посвященная пре- и перинатальной патологии, имеет множество учебных макропрепаратов, которые описывают синдром VACTERL. На их примере мы обсудим каждый характерный дефект развития.

Ключевые слова: плод, VACTERL, врожденный дефект


Курчанова Ю.В., Ивантеева Ю.И., Гаргин В.В.


Стаття присвячена синдрому VACTERL - закономірно об'єднаним вродженим патологіям розвитку. Для постановки синдрому необхідна наявність не менше трьох з наступних дефектів: аномалії хребта, анальна атрезія, пороки серця, трахеостравоходний свищ, ниркові аномалії і аномалії кінцівок. Музейна колекція кафедри патологічної анатомії ХНМУ, присвячена пре- і перинатальній патології, має велику кількість навчальних макропрепаратів, які описують синдром VACTERL. На їхньому прикладі ми обговоримо кожен характерний дефект розвитку.

Ключові слова: плід, VACTERL, вроджений дефект


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